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v4.1 Fusion X
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Atlantoaxial Instability — Pediatric & RA

Causes: congenital anomalies (Down syndrome), os odontoideum, trauma, and rheumatoid arthritis with transverse ligament incompetence. Measure atlantodental interval (ADI): >3 mm in adults or >5 mm in children suggests instability; consider dynamic flexion–extension views. Symptoms: neck pain, myelopathy signs, vertebrobasilar symptoms; intubation risks in RA. Surgery: posterior C1–C2 fusion (Goel‑Harms C1 lateral mass–C2 pedicle/pars screws) ± transarticular screws; consider odontoidectomy for irreducible ventral compression. Screen at‑risk pediatric/RA patients before anesthesia/surgery.

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Causes: congenital anomalies (Down syndrome), os odontoideum, trauma, and rheumatoid arthritis with transverse ligament incompetence. Measure atlantodental interval (ADI): >3 mm in adults or >5 mm in children suggests instability; consider dynamic flexion–extension views. Symptoms: neck pain, myelopathy signs, vertebrobasilar symptoms; intubation risks in RA. Surgery: posterior C1–C2 fusion (Goel‑Harms C1 lateral mass–C2 pedicle/pars screws) ± transarticular screws; consider odontoidectomy for irreducible ventral compression. Screen at‑risk pediatric/RA patients before anesthesia/surgery.
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