Orthonotes
Orthonotes
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v3.0 Fusion
v3.0 Fusion
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Fibrous Dysplasia — Shepherd’s Crook

Developmental fibro‑osseous lesion replacing normal bone with fibrous tissue. Types: monostotic (70%), polyostotic; associated with McCune–Albright (café‑au‑lait, endocrine). X‑ray: ground‑glass appearance, expansion, cortical thinning; Shepherd’s crook deformity of proximal femur. Histology: irregular woven bone trabeculae (‘Chinese letters’) in fibrous stroma. Treatment: bisphosphonates for pain, corrective osteotomies, internal fixation for deformity.

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Developmental fibro‑osseous lesion replacing normal bone with fibrous tissue. Types: monostotic (70%), polyostotic; associated with McCune–Albright (café‑au‑lait, endocrine). X‑ray: ground‑glass appearance, expansion, cortical thinning; Shepherd’s crook deformity of proximal femur. Histology: irregular woven bone trabeculae (‘Chinese letters’) in fibrous stroma. Treatment: bisphosphonates for pain, corrective osteotomies, internal fixation for deformity.
MCQs

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Question 1

What is the most common type of fibrous dysplasia?

Question 2

Which of the following is a characteristic radiological finding in fibrous dysplasia?

Question 3

What is the characteristic deformity associated with fibrous dysplasia of the proximal femur?

Question 4

Which genetic mutation is commonly associated with fibrous dysplasia?

Question 5

What is the main histological feature of fibrous dysplasia?

Question 6

Which syndrome is characterized by polyostotic fibrous dysplasia, café-au-lait spots, and endocrine abnormalities?

Question 7

What treatment is commonly used for pain management in fibrous dysplasia?

Question 8

Which of the following features is least likely to be associated with fibrous dysplasia?

Question 9

Which type of fibrous dysplasia is most likely to undergo malignant transformation?

Question 10

What is the typical clinical presentation of fibrous dysplasia in the proximal femur?