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Madelung Deformity

Congenital or developmental deformity due to premature closure of ulnar volar physis of distal radius. More common in adolescent females; associated with Léri-Weill dyschondrosteosis, Turner syndrome. Clinical: wrist pain, cosmetic deformity, limited pronation/supination. X-ray: increased volar and ulnar tilt of distal radius, carpal wedging, positive ulnar variance. Treatment: mild—observation; severe—physiolysis, corrective osteotomy, ulnar shortening.